European Journal of Anatomy

Official Journal of The Spanish Society of Anatomy
Cover Volume 24 - Number 2
Eur J Anat, 24 (2): 155-159 (2020)

Crossed hemi-hyperplasia with hemi-megalencephaly An unusualsyndromic presentation

Alok Sharma1, Namita Sharma2, Ashutosh Sharma3

1Department of Plastic and Reconstructive Surgery, DY Patil Medical College and Hospital, Pimpri, Pune, Maharash-tra, India 411018, 2Department of Anatomy, Bharati Vidyapeeth Deemed University, Dental College and Hospital, Pu-ne, Maharashtra, India 411043, 3Primary Health Care Centre, Nasrapur, Pune, Maharashtra, India

ABSTRACT Hemimegalencephaly is a rare disorder which may present alone or be associated with hemicor-poral gigantism. However, an association with crossed hemicorporal gigantism involving different upper and lower halves of the body along with se-lective visceromegaly is, so far, unreported in liter-ature.A 14-year-old male presented with a crossed variety of hemi-gigantism associated with a mild form of hemimegalencephaly affecting the left cer-ebral and cerebellar hemispheres. On ultrasound, left renomegaly was noted, though no pathology or dysfunction of the organ could be demonstrated.This case merited a report due to an unusual presentation that defies explanations offered so far for the condition.

Keywords: Hemimegalencephaly Localized gigantism Renomegaly

European Journal of anatomy
ISSN 2340-311X (Online)